Tiglylcarnitine被发现和乳糜泻，线粒体乙酰辅酶A硫代酶(T2)缺乏症有关。
CAS：64681-36-3
分子式：C12H21NO4
分子量：243.3
纯度：98%
存储：Store at -20°C

Background:

Tiglyl carnitine is found to be associated with celiac disease and mitochondrial acetoacetyl-CoA thiolase (T2) deficiency.

[1]. Fukao T, et al. The mitochondrial acetoacetyl-CoA thiolase (T2) deficiency in Japanese patients: urinary organic acid and blood acylcarnitine profiles under stable conditions have subtle abnormalities in T2-deficient patients with some residual T2 activity. J Inherit Metab Dis. 2003;26(5):423-31.