长链烯脂酰辅酶A脱氢酶抗体

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长链烯脂酰辅酶A脱氢酶抗体

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Anti-HADHA
Anti-hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha Antibody

靶标：

HADHA

产品别名：

ECHA； GBP； HADH； LCEH； LCHAD； MTPA； TP-ALPHA； HADHA； hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha； hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha； trifunctional enzyme subunit alpha, mitochondrial； 3-ketoacyl-Coenzyme A (CoA) thiolase, alpha subunit； 3-oxoacyl-CoA thiolase； 78 kDa gastrin-binding protein； gastrin-binding protein； hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit； hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), alpha subunit； long-chain 2-enoyl-CoA hydratase； long-chain-3-hydroxyacyl-CoA dehydrogenase； mitochondrial long-chain 2-enoyl-Coenzyme A (CoA) hydratase, alpha subunit； mitochondrial long-chain L-3-hydroxyacyl-Coenzyme A (CoA) dehydrogenase, alpha subunit； mitochondrial trifunctional enzyme, alpha subunit； mitochondrial trifunctional protein, alpha subunit； monolysocardiolipin acyltransferase；长链烯脂酰辅酶A脱氢酶；

背景信息：

This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. [provided by RefSeq, Jul 2008],