丙酰辅酶A羧化酶α(PCCa)抗体

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丙酰辅酶A羧化酶α(PCCa)抗体

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丙酰辅酶A羧化酶α链抗体
Anti-PCCA

靶标：

PCCA

产品别名：

PCCA； propionyl-CoA carboxylase subunit alpha； propionyl-CoA carboxylase subunit alpha； propionyl-CoA carboxylase alpha chain, mitochondrial； PCCase alpha subunit； pccA complementation group； propanoyl-CoA:carbon dioxide ligase alpha subunit； propionyl CoA carboxylase, alpha polypeptide； propionyl Coenzyme A carboxylase, alpha polypeptide； propionyl-CoA carboxylase alpha subunit；丙酰辅酶A羧化酶α(PCCa)；丙酰辅酶A羧化酶α链；

背景信息：

The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene.