基因名：
CFP
产品别名：
BFD； PFC； PFD； PROPERDIN； CFP； complement factor properdin； complement factor properdin； properdin； complement factor P； properdin P factor, complement； P因子/备解素； 补体因子P(CFP)；
背景信息：
A positive regulator of the alternate pathway of complement. It binds to and stabilizes the C3- and C5-convertase enzyme complexes.
Involvement in disease:Defects in CFP are the cause of properdin deficiency (PFD). PFD results in higher susceptibility to bacterial infections; especially to meningococcal infections. Three phenotypes have been reported: complete deficiency (type I), incomplete deficiency (type II), and dysfunction of properdin (type III).
