基因名：
Mccc2
产品别名：
CG3267； Dmel\CG3267； FBgn0042083； MCCC2_DROME； l(2)4524； Mccc2； Methylcrotonoyl-CoA carboxylase 2； Methylcrotonoyl-CoA carboxylase 2； Methylcrotonoyl-CoA carboxylase 2； CG3267-PA； Mccc2-PA； MCCC2蛋白； 甲基丁烯酰辅酶A羧化酶2(MCCC2)；
背景信息：
This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. [provided by RefSeq, Jul 2008]
